In What Ways Should PAH (arterial) And PVH (venous) Be Treated Differently?
I have read that certain medications meant for one type could actually be harmful if used for the other. Apparently two of my pulmonary doctors have not reached consensus on which of those 2 types of PH I have, leading me to fear bein prescribed the wrong medication.
I'm sharing a few links with you that you might find useful. Basically, it comes down to the pulmonary wedge pressure (calculated during a right heart cath).
"Pulmonary hypertension (PH) is defined by a mean pulmonary artery pressure (mPAP) ≥25 mm Hg. 1 Pulmonary arterial hypertension (PAH), group 1 in the Dana Point Classification, requires a pulmonary wedge pressure (PWP) ≤15 mm Hg. 2, 3 Group 2, pulmonary venous hypertension (PVH), is defined by a PWP >15 mm Hg in addition to an elevated mPAP, and results from elevation in postcapillary pressure attributable to left ventricular (LV) systolic or diastolic dysfunction or left heart valvular disease."
https://www.myphteam.com/resources/pulmonary-ve...
https://www.ahajournals.org/doi/full/10.1161/CI...
https://pulmonaryhypertensionnews.com/pulmonary....
Good question. I actually have 3, b/c I spend a few mo yhs in Florida each winter. When I was diagnosed by the first, where I live in RI, he told me that your standard all-purpose pulmonologist is not fully trained in PH, since it is rare and there are so many standard respiratory disorders. He said I need someone who deals ONLY in PH. I was astonished not to find one near me in FL, where there are so many specialists. Lo and behold, a Boston specialist has an office also in East Providence, RI, only a half hour's drive away. I figure I need all the help I can get! I am struck by how many in our PH group say that their pulmonoligists seem to take a wait-and-see approach, or seem reluctant to prescribe meds. It seems to confirm that there's a lot still to learn about this disease, and that we all need to advocate for ourselves!!
@A myPHteam Member I so agree. There is so much to be learned about this disease. I'm fortunate. My pulmonologist is a PH specialist. My cardiologist readily admitted he is not qualified to manage PAH. I'm also baffled by the "wait and see" philosophy of some physicians. Within a week of diagnosis, I started my first PAH medication. My physician advised treating PAH as aggressively as possible as long as I could tolerate the medications.
I see a cardiologist who specializes in PAH. I recommend finding one near you. My regular cardiologist recommended one. He is great. My pulmonologist didn't even diagnose me.
Treatments for Pulmonary Arterial Hypertension (PAH) and Pulmonary Venous Hypertension (PVH) differ significantly due to their distinct underlying causes:
Treating PAH
- Medications:
- Phosphodiesterase 5 inhibitors (e.g., sildenafil) act as vasodilators to open up blood vessels.
- Endothelin receptor antagonists Show Full Answer
What Is Pre And Post Capirally Hypertension
What Causes Ph
PAH Vs PVH - Do You Know The Difference?